Musculoskeletal system and connective tissue (M00-M99).
- Other vasculitides (inflammatory rheumatic diseases characterized by a propensity for inflammation of (usually) arterial blood vessels)
- Granulomatosis with polyangiitis (GPA), formerly Wegener’s granulomatosis.
- Collagenoses (group of autoimmune diseases associated with changes in connective tissue) – especially Systemic Lupus Erythematosus (SLE).
- Polyarteritis nodosa (PAN, synonyms: Kussmaul-Maier disease, panarteritis nodosa; M30.0) – is a vasculitis of the middle arteries, which belongs to the group of autoimmune diseases