Polymyositis: Classification

Polymyositis (inflammatory disease of the muscles) is classified as follows:

Form Frequency
Primary idiopathic (without identifiable cause) polymyositis 34 %
Primary idiopathic dermatomyositis* 29 %
Polymyositis/dermatomyositis associated with malignant tumors (concomitant disease of cancer) 9%
Polymyositis/dermatomyositis with vasculitis (inflammation of blood vessels) in childhood 7 %
Polymyositis/dermatomyositis in collagenoses (overlap-group/overlap syndromes). 21 %

* Dermatomyositis = polymyositis involving the skin.