Differential diagnoses in general
- Vasculitis, unspecified
Eosinophilic granulomatosis with polyangiitis (EGPA), formerly Churg-Strauss syndrome (CSS)
Musculoskeletal system and connective tissue (M00-M99).
- Other vasculitides (inflammatory rheumatic diseases characterized by a propensity for inflammation of the (usually) arterial blood vessels)
Neoplasms – tumor diseases (C00-D48).
- Hypereosinophilic syndrome (HES; Idiopathic hypereosinophilic syndrome) – unexplained disease; characteristics (high-grade, persistent blood and bone marrow eosinophilia (eosinophilia > 1500/ul in blood for > 6 months) and associated organ dysfunction.
Granulomatosis with polyangiitis (GPA), formerly Wegener’s granulomatosis
Infectious and parasitic diseases (A00-B99).
- Upper respiratory tract diseases, unspecified
- Pulmonary diseases, unspecified
Musculoskeletal system and connective tissue (M00-M99).
- Other vasculitides (inflammatory rheumatic diseases characterized by a tendency to inflammation of the (mostly) arterial blood vessels).
Isolated leukocytoclastic cutaneous vasculitis
Blood, blood-forming organs – immune system (D50-D90).
- Schönlein-Henoch purpura (mostly younger patients).
Skin and subcutaneous tissue (L00-L99)
- Leukocytoclastic vasculitis in collagenoses and cryoglobulinemias.
- Steven-Johnson syndrome (synonyms: dermatostomatitis Baader, Fiessinger-Rendu syndrome) – infectious or drug allergic skin disease.
- Urticarial vasculitis with additional burning and itching urticarial (caused by a vascular reaction of the skin with localized increase in vascular permeability, which is clinically manifested in erythema (areal skin redness) and wheal formation) exanthema (skin rash) in the development of efflorescences.
Musculoskeletal system and connective tissue (M00-M99).
- Systemic juvenile chronic arthritis
- Other small vessel vasculitides.
Neoplasms (C00-D48)
- Hematopoietic neoplasms – malignant neoplasms affecting hematopoiesis.
Kawasaki syndrome (MCLS)
Infectious and parasitic diseases (A00-B99).
- Infectious mononucleosis (synonyms: Pfeiffer glandular fever, Pfeiffer’s glandular fever).
- SARS-CoV-2 (synonyms: novel coronavirus (2019-nCoV); 2019-nCoV (2019-novel coronavirus; coronavirus 2019-nCoV); Wuhan coronaviru) – this respiratory infection with SARS-CoV-2 results in atypical pneumonia (pneumonia), which is called COVID-19 (Engl. coronavirus disease 2019, coronavirus disease-2019) has received; lethality (mortality rate) 2-3%.
- Scarlet fever
Microscopic polyangiitis (MPA)
Musculoskeletal system and connective tissue (M00-M99).
- Other vasculitides (inflammatory rheumatic diseases characterized by a propensity for inflammation of (usually) arterial blood vessels)
- Granulomatosis with polyangiitis (GPA), formerly Wegener’s granulomatosis.
- Collagenoses (group of autoimmune diseases associated with changes in connective tissue) – especially Systemic Lupus Erythematosus (SLE).
- Polyarteritis nodosa (PAN, synonyms: Kussmaul-Maier disease, panarteritis nodosa; M30.0) – is a vasculitis of the middle arteries, which belongs to the group of autoimmune diseases
Polyarteritis nodosa (PAN; panarteritis nodosa)
Skin and subcutaneous tissue (L00-L99).
- Drug and viral exanthema
- Microscopic polyangiitis (MPA)
- Pyoderma gangraenosum (synonym: ulcerative dermatitis) – painful disease of the skin in which ulceration or ulceration (ulceration or ulceration) and gangrene (tissue death due to reduced blood flow or other damage) occur over a large area, usually in one spot
Musculoskeletal system and connective tissue (M00-M99).
- Lupus erythematosus
- Other vasculitides
Neoplasms (C00-D48)
- Hematopoietic neoplasms – malignant neoplasms affecting hematopoiesis.
Schönlein-Henoch purpura
Blood, blood-forming organs – immune system (D50-D90).
- Hemolytic uremic syndrome (HUS) – triad of microangiopathic hemolytic anemia (MAHA; form of anemia in which erythrocytes (red blood cells) are destroyed), thrombocytopenia (abnormal reduction in platelets/platelets), and acute kidney injury (AKI); Mostly occurring in children in the context of infections; most common cause of acute renal failure requiring dialysis in childhood.
- Thrombocytopenia (reduction of blood platelets), idiopathic (without apparent cause).
Cardiovascular system (I00-I99).
- Other vasculitides (vascular inflammation).
Infectious and parasitic diseases (A00-B99).
- Meningococcal sepsis (blood poisoning caused by the bacterium Neisseria meningitidis).
Musculoskeletal system and connective tissue (M00-M99).
Neoplasms – tumor diseases (C00-D48)
- Leukemia (blood cancer)