Bernard-Soulier Syndrome: Causes, Symptoms & Treatment
Bernard-Soulier syndrome, also known as hemorrhagic platelet dystrophy or BSS, is an extremely rare bleeding disorder. BSS is inherited in an autosomal recessive manner. The syndrome itself is classified as one of the so-called plateletopathies. To date, just one hundred cases have been documented; however, the disease course is positive. What is Bernard-Soulier syndrome? Bernard-Soulier … Bernard-Soulier Syndrome: Causes, Symptoms & Treatment