Blood, blood-forming organs-immune system (D50-D90).
- Willebrand-Jürgens syndrome (synonyms: von Willebrand-Jürgens syndrome; von Willebrand syndrome, vWS) – most common congenital disease with increased bleeding tendency; disease is predominantly transmitted autosomal-dominantly with variable penetrance, type 2 C and type 3 are inherited autosomal-recessively; there is a quantitative or qualitative defect of the von Willebrand factor; this impairs, among other things Among other things, the platelet aggregation (aggregation of platelets) and their cross-linking and / or (depending on the manifestation of the disease) the degradation of coagulation factor VIII is insufficiently inhibited.
- Bleeding tendency due to factor deficiency, unspecified.
Skin and subcutaneous (L00-L99)
- Nevus fuscocaeruleus: blue-green or blue-gray patchy accumulation of melanocytes (pigment-forming cells of the skin) expressed in varying size, shape, intensity, and localization (coccyx and buttocks); increase in size as well as intensity in the first year of life, spontaneous regression in the following years; by the age of five, 97% of the changes are no longer detectable; occurrence in central and northern European children in 1-10% of cases.